منابع مشابه
Classic diseases revisited Progressive supranuclear palsy (Steele-Richardson-Olszewski disease)
Progressive supranuclear palsy is a neurodegenerative disease which aVects the brainstem and basal ganglia. Patients present with disturbance of balance, a disorder of downward gaze and L-DOPA-unresponsive parkinsonism and usually develop progressive dysphagia and dysarthria leading to death from the complications of immobility and aspiration. Treatment remains largely supportive but, potential...
متن کاملThe prevalence of progressive supranuclear palsy (Steele-Richardson-Olszewski syndrome) in the UK.
We performed a study to estimate the point prevalence of progressive supranuclear palsy (PSP) in the UK at national, regional and community levels. A 'Russian doll' design was used in which the population denominator for each of the three studies was successively smaller, whilst the method of case ascertainment became increasingly more rigorous. The NINDS-SPSP (National Institute of Neurologica...
متن کاملA 72‐year‐old with eyelid opening apraxia in Steele–Richardson–Olszewski syndrome
In our patient with Steele-Richardson-Olszewski syndrome presenting with apraxia of eyelid opening, there is a possibility to be readily confused with conditions presenting in similar pattern such as blepharospasm and eyelid ptosis. Therefore, it is essential to correlate the clinical findings with electromyographic recordings and dopamine transporter scan (DaT).
متن کاملNocturnal and respiratory disturbances in Steele-Richardson-Olszewski syndrome (progressive supranuclear palsy).
Respiratory and sleep disturbances may be important causes of morbidity in Steele-Richardson-Olszewski syndrome but the frequency and character of nocturnal abnormalities remains uncertain. A prospective study of 11 patients with Steele-Richardson-Olszewski syndrome and age-matched control subjects was undertaken using clinical assessments, a structured sleep questionnaire, spirometry, static m...
متن کاملThe nucleus raphe interpositus in the Steele-Richardson-Olszewski syndrome (progressive supranuclear palsy).
As the integrity of the omnipause neurons located in the nucleus raphe interpositus is a prerequisite of normal ocular motility, cell and neurofibrillary tangle densities were determined in 13 Steele-Richardson-Olszewski syndrome (SROS) cases [eight with supranuclear gaze palsy (SGP) and five without] and six controls. Compared with normal controls, cases with SGP were associated with approxima...
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ژورنال
عنوان ژورنال: Medical Journal of Dr. D.Y. Patil University
سال: 2013
ISSN: 0975-2870
DOI: 10.4103/0975-2870.114671